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Ophthalmology and Visual Sciences

Congenital aniridia

Congenital aniridias

Category(ies): Cornea, Inherited Eye Disease
Contributor: Jesse Vislisel, MD
Photographers: Cindy Montague, CRA

Congenital aniridia is a hereditary disease most commonly with autosomal dominant inheritance. These slit lamp photographs show iris hypoplasia and corneal scarring in a patient with congenital aniridia. This patient underwent cataract surgery and has 3-piece posterior chamber intraocular lenses in both eyes which are easily visible with retroillumination.

 congenital aniridia has 3-piece posterior chamber intraocular lenses
This patient with congenital aniridia has 3-piece posterior chamber intraocular lenses in both eyes
 congenital aniridia has 3-piece posterior chamber intraocular lenses
This patient with congenital aniridia has 3-piece posterior chamber intraocular lenses in both eyes
 congenital aniridia retroillumination
They are seen on retroillumination
 congenital aniridia retroillumination
They are seen on retroillumination